Product Name: HADHA Polyclonal Antibody, Biotin Conjugated
Applications: WB, IHC-P
Reactivity: Human, Mouse, Rat
Conjugation: Biotin
Host: Rabbit
Sourcr: KLH conjugated synthetic peptide derived from human HADHA
Clonality: Polyclonal
CAS NO: 475205-49-3
Product: Nebivolol (hydrochloride)
Isotype: IgG
Concentration: 1ug/ul
Purification: Purified by Protein A.
Storage: Aqueous buffered solution containing 1% BSA, 50% glycerol and 0.09% sodium azide. Store at 4°C for 12 months.
Synonyms: HADHA; LCHAD; ECHA; GBP; HADH; LCEH; LCHAD; MTPA; TP-ALPHA; 3 ketoacyl Coenzyme A CoA thiolase alpha subunit; 3 oxoacyl CoA thiolase; 78 kDa gastrin binding protein; GBPv HADHv Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase trunctional protein alpha subunit; LCHAD; Mitochondrial long chain 2 enoyl Coenzyme A CoA hydratase alpha subunit; Mitochondrial long chain L 3 hydroxyacyl Coenzyme A dehydrogenase alpha; Mitochondrial trunctional enzyme alpha subunit; Mitochondrial trunctional protein alpha subunit; MTPA; Thiolase/enoyl Coenzyme A hydratase trunctional protein alpha subunit; TP ALPHA; Trunctional enzyme subunit alpha mitochondrial precursor.
Background: This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008].
PubMed ID:http://www.ncbi.nlm.nih.gov/pubmed/20038517?dopt=Abstract
